Arrhythmogenic Right Ventricular Cardiomyopathy Accompanied by Chronic Myocarditis

研究成果: ジャーナルへの寄稿学術論文査読

抄録

Patients with arrhythmogenic right ventricular cardiomyopathy (ARVC) classically present with ventricular arrhythmias and less commonly heart failure. ARVC is an inherited cardiomyopathy and generally based on a variant of desmosomal genes. Recently, the association between myocardial inflammation and ARVC has been a matter of great concern. We encountered a patient with ARVC who had a desmoglein-2 mutation with advanced right ventricular failure accompanying a preserved left ventricular function. Concomitant right ventricular myocarditis was detected four years after the diagnosis of ARVC. ARVC and myocarditis might have a deep pathophysiological association, at least in some cases.

本文言語英語
ジャーナルInternal Medicine
DOI
出版ステータス印刷前の電子出版 - 2022/03/26

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