Expression of Myeloid-Related Protein-8 and -14 in Patients With Acute Kawasaki Disease

Keiich Hirono, Dirk Foell, Yanlin Xing, Sachiko Miyagawa-Tomita, Fei Ye, Martina Ahlmann, Thomas Vogl, Takeshi Futatani, Chen Rui, Xianyi Yu, Kazuhiro Watanabe, Sayaka Wanatabe, Shinichi Tsubata, Keiichiro Uese, Ikuo Hashimoto, Fukiko Ichida*, Makoto Nakazawa, Johannes Roth, Toshio Miyawaki

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

59 Scopus citations

Abstract

Objectives: This study investigated patients with acute Kawasaki disease (KD) to validate myeloid-related protein (MRP)-8/MRP-14 as a marker of disease activity and severity of coronary artery lesion development. Background: Both MRP-8 and -14, which are S100-proteins secreted by activated neutrophils and monocytes, bind specifically to endothelial cells and induce thrombogenic and inflammatory responses in a variety of disease conditions. Methods: We investigated 61 patients with acute KD and examined sequential changes in serum levels of MRP-8/MRP-14, messenger ribonucleic acid (mRNA) expression of MRP-8 and -14 in circulating granulocytes and monocytes, and amounts of MRP-8/MRP-14 bound to circulating endothelial cells. Results: The serum MRP-8/MRP-14 levels as well as mRNA expressions of MRP-8 and -14 in granulocytes were strongly upregulated during the early stage of acute KD, and decreased dramatically within 24 h of intravenous immune globulin therapy (p < 0.05) in 45 responders. In contrast, in 16 nonresponders both of these increased after the initial treatment. The number of MRP-8/MRP-14-positive circulating endothelial cells was higher in patients with acute KD than in control patients and increased significantly by 2 weeks after the onset of KD, especially in patients in whom coronary artery lesions developed. Conclusions: We show for the first time that MRP-8/MRP-14 are exclusively secreted by granulocytes in patients with acute KD, and intravenous immune globulin treatment suppresses their gene expression. Serum levels of MRP-8/MRP-14 may be useful markers of disease activity, and the levels of MRP-8/MRP-14-positive circulating endothelial cell may predict the severity of vasculitis, confirming an important role for distinct inflammatory reactions in endothelium.

Original languageEnglish
Pages (from-to)1257-1264
Number of pages8
JournalJournal of the American College of Cardiology
Volume48
Issue number6
DOIs
StatePublished - 2006/09/19

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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